MAAs occur in myositis but also in other autoimmune diseases. They help identify overlap syndromes and predict complications.

Autoantibody
Associated ConditionsFeaturesManagement
Anti‑PM/Scl
Polymyositis–scleroderma overlapILD, Raynaud, mechanic’s hands, calcinosisMonitor lungs; overlap responds to immunosuppression
Anti Ku
Myositis + systemic sclerosisILD, arthritis, esophageal involvementTreat both muscle and connective tissue disease
Anti U3 RNP (Fibrillarin)
Myositis + diffuse systemic sclerosisSevere systemic involvementRequires multi system monitoring
Anti Ro/SSA
Myositis, Sjögren’s, lupusOften co occurs with antisynthetase antibodiesMay increase ILD risk; monitor lungs
Anti U1 RNP
Mixed connective tissue disease (MCTD)Raynaud, arthritis, mild myositisTreat overlap features; generally good prognosis
Anti RNP70
MCTD spectrumRaynaud, arthritis, mild myositisOverlap focused care
Anti La/SSB
Sjögren’s, lupus, overlap myositisSicca symptoms, mild myositisSupportive care + immunosuppression as needed

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